Features of management of patients with arrhythmogenic right ventricular cardiomyopathy

• Duplyakov Dmitriy V.
• Yugzova A.V.
• Tuturov A.O.

Abstract

Arrhythmogenic cardiomyopathy of the right ventricle is a poorly studied disease characterized by structural anomalies of the right ventricle in combination with severe rhythm disturbances. The structural aspects of the pathology are associated with fibrous-fatty degeneration of cardiomyocytes, which often leads to dilation of the right ventricle, thinning of its wall and the development of ventricular tachyarrhythmias. Arrhythmogenic cardiomyopathy is referred to a group of genetic diseases. Now there is no information about other factors affecting the development of pathology. In this regard, diagnosis is possible only at the stages of clinical manifestations, and treatment is aimed only at eliminating symptoms and isn't radical.

The aim of this work is to study and describe the current principles of diagnosis and treatment of arrhythmogenic cardiomyopathy of the right ventricle. Analysis of the results of fundamental research is necessary to identify promising tactics of management of patients suffering from this pathology. Optimization of earlier studies is necessary to summarize the intermediate results of progress in understanding the pathophysiology of arrhythmogenic cardiomyopathy. Currently, arrhythmogenic cardiomyopathy has a well-functioning system of clinical diagnosis and pathogenetic treatment, but further study of this disease is necessary to determine a radical approach.

Keywords:arrhythmogenic cardiomyopathy, right ventricle, dysplasia, arrhythmias, management tactics

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